95187

Methylmalonyl-L-carnitine lithium salt

analytical standard

• Synonim(y): (2R)-3-Carboxy-2-(2-carboxy-1-oxopropoxy)-N,N,N-trimethyl-1-propanaminium inner salt lithium salt, O-Methylmalonyl-L-carnitine lithium salt
• Wzór empiryczny (zapis Hilla): C₁₁H₁₉NO₆ · xLi⁺
• Numer CAS: 251976-17-7
• Masa cząsteczkowa: 261.27 (free acid basis)
• UNSPSC Code: 41116107

Właściwości

• grade: analytical standard
• Quality Level: 100
• assay: ≥90.0% (HPLC)
• form: solid
• optical activity: [α]/D -33.0±2.0°, c = 0.1 in H₂O
• shelf life: limited shelf life, expiry date on the label
• application(s): clinical testing
• storage temp.: 2-8°C
• SMILES string: C[N+](C)(C)C[C@H](OC(C(C)C(O)=O)=O)CC([O-])=O

Opis

Biochem/physiol Actions

O-Methylmalonyl-L-carnitine belongs to the class of acyl carnitines. Acyl carnitines contain a fatty acid with the carboxylic acid attached to carnitine through an ester bond. The level of methylmalonyl carnitine has been found to be increased in patients with methylmalonuric aciduria (MMA), one of the most frequent organic acidurias caused by enzymatic defects involved in the catabolism of branched-chain amino acids.

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Informacja o środkach bezpieczeństwa

• Klasa składowania: 11 - Combustible Solids
• wgk: WGK 3
• flash_point_f: Not applicable
• flash_point_c: Not applicable