95187
Methylmalonyl-L-carnitine lithium salt
analytical standard
동의어(들):
(2R)-3-Carboxy-2-(2-carboxy-1-oxopropoxy)-N,N,N-trimethyl-1-propanaminium inner salt lithium salt, O-Methylmalonyl-L-carnitine lithium salt
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모든 사진(1)
About This Item
실험식(Hill 표기법):
C11H19NO6 · xLi+
CAS Number:
Molecular Weight:
261.27 (free acid basis)
UNSPSC 코드:
41116107
추천 제품
![[(3R)-3-Hydroxybutyryl]-L-carnitine analytical standard](/deepweb/assets/sigmaaldrich/product/structures/658/500/ff9570f8-a346-4077-9983-d0e67400bf47/640/ff9570f8-a346-4077-9983-d0e67400bf47.png)
![[(3R)-3-Hydroxyhexanoyl]-L-carnitine analytical standard](/deepweb/assets/sigmaaldrich/product/structures/529/281/b2c430b9-0eaf-42c2-9f83-291338e64187/640/b2c430b9-0eaf-42c2-9f83-291338e64187.png)
Grade
analytical standard
Quality Level
분석
≥90.0% (HPLC)
양식
solid
광학 활성
[α]/D -33.0±2.0°, c = 0.1 in H2O
유통기한
limited shelf life, expiry date on the label
응용 분야
clinical testing
저장 온도
2-8°C
SMILES string
C[N+](C)(C)C[C@H](OC(C(C)C(O)=O)=O)CC([O-])=O
생화학적/생리학적 작용
O-Methylmalonyl-L-carnitine belongs to the class of acyl carnitines. Acyl carnitines contain a fatty acid with the carboxylic acid attached to carnitine through an ester bond. The level of methylmalonyl carnitine has been found to be increased in patients with methylmalonuric aciduria (MMA), one of the most frequent organic acidurias caused by enzymatic defects involved in the catabolism of branched-chain amino acids.
Storage Class Code
11 - Combustible Solids
WGK
WGK 3
Flash Point (°F)
Not applicable
Flash Point (°C)
Not applicable
가장 최신 버전 중 하나를 선택하세요:
William R Wikoff et al.
Clinical chemistry, 53(12), 2169-2176 (2007-10-24)
We applied untargeted mass spectrometry-based metabolomics to the diseases methylmalonic acidemia (MMA) and propionic acidemia (PA). We used a screening platform that used untargeted, mass-based metabolomics of methanol-extracted plasma to find significantly different molecular features in human plasma samples from
Cristiano Rizzo et al.
Clinica chimica acta; international journal of clinical chemistry, 429, 30-33 (2013-11-26)
Methylmalonic aciduria (MMA) is one of the most frequent organic acidurias, a class of diseases caused by enzymatic defects mainly involved in the catabolism of branched-chain amino acids. Recently, mild MMA and C4-dicarboxylyl-carnitine (C4DC-C) accumulation have been reported in patients
활성 필터
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