91298

3-Hydroxyisovaleryl-L-carnitine

analytical standard

• 동의어(들): (2R)-3-Carboxy-2-(3-hydroxy-3-methyl-1-oxobutoxy)-N,N,N-trimethyl-1-propanaminium inner salt
• 실험식(Hill 표기법): C₁₂H₂₃NO₅
• CAS Number: 99159-87-2
• Molecular Weight: 261.31
• Beilstein: 10549761
• UNSPSC 코드: 41116107
• NACRES: NA.24

속성

• Grade: analytical standard
• Quality Level: 100
• 분석: ≥90.0% (HPLC)
• 광학 활성: [α]/D -17.0±2.0°, c = 0.1 in H₂O
• 유통기한: limited shelf life, expiry date on the label
• 불순물: ≤15% water (calc. on elemental analysis)
• 응용 분야: clinical testing
• 형식: neat
• 저장 온도: 2-8°C
• SMILES string: C[N+](C)(C)C[C@H](OC(CC(C)(O)C)=O)CC([O-])=O
• InChI: 1S/C12H23NO5/c1-9(2)6-11(16)18-12(17,7-10(14)15)8-13(3,4)5/h9,17H,6-8H2,1-5H3
• InChI key: DHRNMNHPSWBJEN-UHFFFAOYSA-N

설명

생화학적/생리학적 작용

3-Hydroxyisovaleryl-L-carnitine is an endogenous metabolite that can result from impairment in the leucine catabolic pathway. 3-Hydroxyisovaleryl-L-carnitine was observed in plasma and urine of patient with isolated 3-methylcrotonyl-CoA carboxylase deficiency and is used as biomarker of biotin deficiency in humans and other metabolic disorders.

추천 제품

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안전성 정보

• Storage Class Code: 11 - Combustible Solids
• WGK: WGK 3
• Flash Point (°F): Not applicable
• Flash Point (°C): Not applicable