Direkt zum Inhalt
Merck

The occurrence of gamma-glutamylphenylalanine in the urine of newborn phenylketonurics.

Clinica chimica acta; international journal of clinical chemistry (1979-06-15)
H Peck, R J Pollitt
PMID466810
ZUSAMMENFASSUNG

The urine of untreated phenylketonurics in the first weeks of life contains gamma-glutamylphenylalanine (0.07--0.69 mmol/g creatinine, 12 samples) visible on the normal 2-dimensional electrophoreto-chromatogram. This compound is less prominent or absent when urine from older untreated phenylketonurics is examined and is not seen in normal urine.

MATERIALIEN
Produktnummer
Marke
Produktbeschreibung

Sigma-Aldrich
L-Leucin, from non-animal source, meets EP, JP, USP testing specifications, suitable for cell culture, 98.5-101.0%
Sigma-Aldrich
L-Leucin, reagent grade, ≥98% (HPLC)
Sigma-Aldrich
L-Phenylalanin, from non-animal source, meets EP, JP, USP testing specifications, suitable for cell culture, 98.5-101.0%
Sigma-Aldrich
L-Valin, from non-animal source, meets EP, JP, USP testing specifications, suitable for cell culture, 98.5-101.0%
Sigma-Aldrich
Phenylessigsäure, 99%
Sigma-Aldrich
Mandelsäure, 99%
Sigma-Aldrich
L-Phenylalanin, BioUltra, ≥99.0% (NT)
SAFC
L-Valin
Sigma-Aldrich
17α-Hydroxyprogesteron, ≥95%
Sigma-Aldrich
Phenylessigsäure, ≥99%, FCC, FG
Sigma-Aldrich
DL-3-Phenyl-milchsäure, ≥98%
Sigma-Aldrich
L-Leucin, BioUltra, ≥99.5% (NT)
Sigma-Aldrich
L-Phenylalanin, reagent grade, ≥98%
Sigma-Aldrich
Phenylbrenztraubensäure, 98%
Sigma-Aldrich
L-Valin, BioUltra, ≥99.5% (NT)
Sigma-Aldrich
L-Leucin, 99%, FG
Sigma-Aldrich
L-Valin, reagent grade, ≥98% (HPLC)
Sigma-Aldrich
L-(−)-3-Phenylmilchsäure, 98%
Sigma-Aldrich
2-Hydroxyphenylessigsäure, ReagentPlus®, 99%
Sigma-Aldrich
3-Hydroxyphenylessigsäure, ≥99%
Supelco
17α-Hydroxyprogesterone solution, 1.0 mg/mL in methanol, ampule of 1 mL, certified reference material, Cerilliant®
Sigma-Aldrich
L-Phenylalanin, 99%, FCC
Supelco
L-Leucin, Pharmaceutical Secondary Standard; Certified Reference Material
Supelco
L-Phenylalanin, Pharmaceutical Secondary Standard; Certified Reference Material
Supelco
L-Valin, Pharmaceutical Secondary Standard; Certified Reference Material
Supelco
L-Leucin, certified reference material, TraceCERT®, Manufactured by: Sigma-Aldrich Production GmbH, Switzerland
Supelco
DL-Mandelsäure, analytical standard
Supelco
L-Phenylalanin, certified reference material, TraceCERT®, Manufactured by: Sigma-Aldrich Production GmbH, Switzerland
Supelco
L-Valin, certified reference material, TraceCERT®, Manufactured by: Sigma-Aldrich Production GmbH, Switzerland