Przejdź do zawartości
Merck

CPS1

carbamoyl-phosphate synthase 1, mitochondrial

Synonimy:
CPSASE1, PHN
Gatunek:
Identyfikator UniProtKB:
Identyfikator genu:
  • Human(1373) Summary: The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.[provided by RefSeq, May 2010]
  • Mouse(227231) carbamoyl-phosphate synthetase 1
  • Rat(497840) carbamoyl-phosphate synthetase 1
  • Horse(100050116) carbamoyl-phosphate synthase 1, mitochondrial
  • sheep(101107584) carbamoyl-phosphate synthase 1, mitochondrial
  • Zebrafish(555623) carbamoyl-phosphate synthase 1, mitochondrial
  • naked mole-rat(101696508) carbamoyl-phosphate synthase 1, mitochondrial
  • chicken(428994) carbamoyl-phosphate synthase 1, mitochondrial
  • domestic guinea pig(100723563) carbamoyl-phosphate synthase 1, mitochondrial
  • dog(488506) carbamoyl-phosphate synthase 1, mitochondrial
  • domestic cat(101099824) carbamoyl-phosphate synthase 1, mitochondrial
  • cow(510506) carbamoyl-phosphate synthase 1, mitochondrial

Custom & Knockdown Gene Products

  • siRNA

    Shop predesigned siRNA that are designed using the proprietary Rosetta Inpharmatics algorithm.

  • shRNA

    Shop the largest, most validated shRNA collection and build your own clone sets.

  • Custom Gene Products

    We offer a comprehensive portfolio of DNA oligos, RNA oligos and predesigned primers.

Small Molecule - Allosteric Modulator

Numer produktu
Opis
Gatunek
N-Carbamyl-L-glutamic acid, ,
Gatunek
human
Carglumic Acid, United States Pharmacopeia (USP) Reference Standard,
Gatunek
human

Antibodies

Numer produktu
Opis
Reaktywność gatunkowa
Zastosowanie
Anti-CPS1 (AB2) antibody produced in rabbit, IgG fraction of antiserum,
Reaktywność gatunkowa
human
Zastosowanie
immunohistochemistry
western blot
Anti-CPS1 antibody produced in rabbit, ,
Reaktywność gatunkowa
human, rat
Zastosowanie
immunohistochemistry
western blot
Anti-CPS1 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Reaktywność gatunkowa
human
Zastosowanie
immunofluorescence
immunohistochemistry

western blot
Anti-CD8a Rabbit Monoclonal Antibody, clone RM395, affinity purified immunoglobulin,
Reaktywność gatunkowa
human
Zastosowanie
immunohistochemistry
western blot

esiRNA

Numer produktu
Opis
Gatunek
MISSION® esiRNA, targeting human CPS1,
Gatunek
human