AGL is a glycogen debrancher enzyme which is involved in glycogen degradation. This enzyme has two independent catalytic activities which occur at different sites on the protein: a 4-alpha-glucotransferase activity and a amylo-1,6-glucosidase activity. Mutations in the AGL gene are associated with glycogen storage disease although a wide range of enzymatic and clinical variability occurs which may be due to tissue-specific alternative splicing.
면역원
AGL (NP_000019, 361-397) This antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide selected from the center region of human AGL.
물리적 형태
Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide.