91298

3-Hydroxyisovaleryl-L-carnitine

analytical standard

• Sinónimos: (2R)-3-Carboxy-2-(3-hydroxy-3-methyl-1-oxobutoxy)-N,N,N-trimethyl-1-propanaminium inner salt
• Fórmula empírica (notación de Hill): C₁₂H₂₃NO₅
• Número de CAS: 99159-87-2
• Peso molecular: 261.31
• Beilstein: 10549761
• Número MDL: MFCD32061910
• Código UNSPSC: 41116107
• NACRES: NA.24

Propiedades

• grado: analytical standard
• Nivel de calidad: 100
• Ensayo: ≥90.0% (HPLC)
• actividad óptica: [α]/D -17.0±2.0°, c = 0.1 in H₂O
• caducidad: limited shelf life, expiry date on the label
• impurezas: ≤15% water (calc. on elemental analysis)
• aplicaciones: clinical testing
• Formato: neat
• temp. de almacenamiento: 2-8°C
• cadena SMILES: C[N+](C)(C)C[C@H](OC(CC(C)(O)C)=O)CC([O-])=O
• InChI: 1S/C12H23NO5/c1-9(2)6-11(16)18-12(17,7-10(14)15)8-13(3,4)5/h9,17H,6-8H2,1-5H3
• Clave InChI: DHRNMNHPSWBJEN-UHFFFAOYSA-N

Descripción

Acciones bioquímicas o fisiológicas

3-Hydroxyisovaleryl-L-carnitine is an endogenous metabolite that can result from impairment in the leucine catabolic pathway. 3-Hydroxyisovaleryl-L-carnitine was observed in plasma and urine of patient with isolated 3-methylcrotonyl-CoA carboxylase deficiency and is used as biomarker of biotin deficiency in humans and other metabolic disorders.

Productos recomendados

Find a digital Reference Material for this product available on our online platform ChemisTwin® for NMR. You can use this digital equivalent on ChemisTwin® for your sample identity confirmation and compound quantification (with digital external standard). An NMR spectrum of this substance can be viewed and an online comparison against your sample can be performed with a few mouseclicks. Learn more here and start your free trial.

Información de seguridad

• Código de clase de almacenamiento: 11 - Combustible Solids
• Clase de riesgo para el agua (WGK): WGK 3
• Punto de inflamabilidad (°F): Not applicable
• Punto de inflamabilidad (°C): Not applicable