72715

Glutaryl-L-carnitine lithium salt

≥98.0% (TLC)

• Sinonimo/i: L-Carnitine lithium glutarate
• Formula empirica (notazione di Hill): C₁₂H₂₁NO₆ · xLi⁺
• Numero CAS: 102636-82-8
• Peso molecolare: 275.30 (free acid basis)
• UNSPSC Code: 41116107
• PubChem Substance ID: 329764299
• NACRES: NA.25

Proprietà

• Nome del prodotto: Glutaryl-L-carnitine lithium salt, ≥98.0% (TLC)
• Quality Segment: 100
• assay: ≥98.0% (TLC)
• form: solid
• optical activity: [α]/D -20±2°, c = 1 in H₂O
• impurities: ≤10% water
• color: white to off-white
• storage temp.: 2-8°C
• SMILES string: C[N+](C)(C)C[C@H](OC(CCCC(O)=O)=O)CC([O-])=O.C
• InChI: 1S/C12H21NO6/c1-13(2,3)8-9(7-11(16)17)19-12(18)6-4-5-10(14)15/h9H,4-8H2,1-3H3,(H-,14,15,16,17)/t9-/m1/s1
• InChI key: NXJAXUYOQLTISD-SECBINFHSA-N

Descrizione

Biochem/physiol Actions

Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction.

Informazioni sulla sicurezza

• Classe di stoccaggio: 11 - Combustible Solids
• wgk: WGK 3
• flash_point_f: Not applicable
• flash_point_c: Not applicable