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ALDH5A1

aldehyde dehydrogenase 5 family, member A1

Synonyme:
SSADH, SSDH
Spezies:
UniProtKB-ID:
Gen-ID:
  • Human(7915) Summary: This protein belongs to the aldehyde dehydrogenase family of proteins. This gene encodes a mitochondrial NAD(+)-dependent succinic semialdehyde dehydrogenase. A deficiency of this enzyme, known as 4-hydroxybutyricaciduria, is a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA). In response to the defect, physiologic fluids from patients accumulate GHB, a compound with numerous neuromodulatory properties. Two transcript variants encoding distinct isoforms have been identified for this gene. [provided by RefSeq, Jul 2008]
  • Mouse(214579) aldhehyde dehydrogenase family 5, subfamily A1
  • Rat(291133) aldehyde dehydrogenase 5 family, member A1
  • naked mole-rat(101723101) aldehyde dehydrogenase 5 family, member A1
  • domestic guinea pig(100735182) aldehyde dehydrogenase 5 family, member A1
  • dog(488246) aldehyde dehydrogenase 5 family, member A1
  • domestic cat(101088238) aldehyde dehydrogenase 5 family, member A1
  • cow(532724) aldehyde dehydrogenase 5 family, member A1
  • Domestic Rabbit(100351836) aldehyde dehydrogenase 5 family, member A1
  • sheep(101107828) aldehyde dehydrogenase 5 family, member A1
  • Zebrafish(565235) aldehyde dehydrogenase 5 family, member A1 (succinate-semialdehyde dehydrogenase)
  • chicken(420818) aldehyde dehydrogenase 5 family, member A1

Custom & Knockdown Gene Products

Antibodies

Produktnummer
Beschreibung
Speziesreaktivität
Anwendung
Anti-ALDH5A1 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution, ab1,
Speziesreaktivität
human
Anwendung
immunohistochemistry
western blot
Anti-ALDH5A1 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution, ab2,
Speziesreaktivität
human
Anwendung
immunofluorescence
immunohistochemistry

western blot

Small Molecule - Inhibitor

Produktnummer
Beschreibung
Spezies
Valproinsäure Natriumsalz, 98%,
Spezies
human
Valproinsäure, Pharmaceutical Secondary Standard; Certified Reference Material,
Spezies
human
Valproinsäure, United States Pharmacopeia (USP) Reference Standard,
Spezies
human
Natriumvalproat, British Pharmacopoeia (BP) Reference Standard,
Spezies
human
Natriumvalproat, European Pharmacopoeia (EP) Reference Standard,
Spezies
human

esiRNA

Produktnummer
Beschreibung
Spezies
MISSION® esiRNA, targeting mouse Aldh5a1,
Spezies
mouse
MISSION® esiRNA, targeting human ALDH5A1,
Spezies
human