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MilliporeSigma

BBOX1

butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1

Synonyms:
BBH, BBOX, G-BBH, gamma-BBH
Species:
Human BBOX1 (8424), Mouse Bbox1 (170442), Rat Bbox1 (64564), dog BBOX1 (476894), chicken BBOX1 (426932), Zebrafish bbox1 (572649), Domestic Rabbit BBOX1 (100356171), sheep BBOX1 (101115823), Horse BBOX1 (100072253), domestic cat BBOX1 (101082182) ...More
UniProtKB ID:
O75936, B2R8L7, D3DQZ1, Q6IBJ2
Gene ID:
  • Human(8424) Summary: This gene encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation. [provided by RefSeq, Jul 2008]
  • Mouse(170442) butyrobetaine (gamma), 2-oxoglutarate dioxygenase 1 (gamma-butyrobetaine hydroxylase)
  • Rat(64564) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • dog(476894) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • chicken(426932) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • Zebrafish(572649) butyrobetaine (gamma), 2-oxoglutarate dioxygenase 1 (gamma-butyrobetaine hydroxylase)
  • Domestic Rabbit(100356171) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • sheep(101115823) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • Horse(100072253) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • domestic cat(101082182) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • naked mole-rat(101702765) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • domestic guinea pig(100724732) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • cow(507159) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1

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Antibodies

Product Number
Description
Species Reactivity
Application
HPA007600
Anti-BBOX1 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Species Reactivity
human
Application
immunohistochemistry
western blot
WH0008424M1
Monoclonal Anti-BBOX1 antibody produced in mouse, clone 6H3, purified immunoglobulin, buffered aqueous solution,
Species Reactivity
human
Application
ELISA
immunohistochemistry
western blot

esiRNA

Product Number
Description
Species
EHU136061
MISSION® esiRNA, targeting human BBOX1,
Species
human