PAH
phenylalanine hydroxylase
Synonyms:
PH, PKU, PKU1
Species:
Human PAH (5053), Mouse Pah (18478), Rat Pah (24616), Zebrafish pah (378962), chicken PAH (408024), dog PAH (475446), domestic cat PAH (101081741), Horse PAH (100053361), cow PAH (510583), sheep PAH (101110405) ...More
UniProtKB ID:
Gene ID:
- Human(5053) Summary: PAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria. [provided by RefSeq, Jul 2008]
- Mouse(18478) phenylalanine hydroxylase
- Rat(24616) phenylalanine hydroxylase
- Zebrafish(378962) phenylalanine hydroxylase
- chicken(408024) phenylalanine hydroxylase
- dog(475446) phenylalanine hydroxylase
- domestic cat(101081741) phenylalanine hydroxylase
- Horse(100053361) phenylalanine hydroxylase
- cow(510583) phenylalanine hydroxylase
- sheep(101110405) phenylalanine hydroxylase
- Domestic Rabbit(100354678) phenylalanine hydroxylase
- domestic guinea pig(100719535) phenylalanine hydroxylase
- naked mole-rat(101705870) phenylalanine hydroxylase
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Small Molecule - Activator
Product Number
Description
Species
Antibodies
Product Number
Description
Species Reactivity
Application
Anti-PAH antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Species Reactivity
human
Application
immunohistochemistry
western blot
western blot
Anti-PAH antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Species Reactivity
human
Application
immunohistochemistry
western blot
western blot
Anti-PAH antibody produced in rabbit, purified immunoglobulin, buffered aqueous solution,
Species Reactivity
human
Application
western blot
Anti-PAH antibody produced in goat, affinity isolated antibody, buffered aqueous solution,
Species Reactivity
human, rat
Application
ELISA
western blot
western blot
Anti-PAH Antibody, clone 1L14 ZooMAb® Rabbit Monoclonal, recombinant, expressed in HEK 293 cells,
Species Reactivity
human, mouse, rat
Application
affinity binding assay
immunofluorescence
immunohistochemistry
western blot
immunofluorescence
immunohistochemistry
western blot
esiRNA
Product Number
Description
Species