50405

2-Methylbutyryl-L-carnitin

≥97.0% (HPLC)

• Synonym(e): (2R)-3-Carboxy-N,N,N-trimethyl-2-(2-methyl-1-oxobutoxy)-1-propanaminium Inneres Salz
• Empirische Formel (Hill-System): C₁₂H₂₃NO₄
• CAS-Nummer: 256928-75-3
• Molekulargewicht: 245.32
• Beilstein: 5946881
• MDL-Nummer: MFCD11975299
• UNSPSC-Code: 41116107
• PubChem Substanz-ID: 329757597
• NACRES: NA.26

Eigenschaften

• product name: 2-Methylbutyryl-L-carnitin, ≥97.0% (HPLC)
• Qualitätsniveau: 100
• Assay: ≥97.0% (HPLC)
• Form: powder or crystals
• Optische Aktivität: [α]/D -20±2°, c = 0.1 in H₂O
• Verunreinigungen: ≤10% water
• Farbe: white to off-white
• Lagertemp.: 2-8°C
• SMILES String: C[N+](C)(C)C[C@H](OC(C(CC)C)=O)CC([O-])=O
• InChI: 1S/C12H23NO4/c1-6-9(2)12(16)17-10(7-11(14)15)8-13(3,4)5/h9-10H,6-8H2,1-5H3/t9?,10-/m1/s1
• InChIKey: IHCPDBBYTYJYIL-QVDQXJPCSA-N

Beschreibung

Biochem./physiol. Wirkung

2-Methylbutyryl-L-carnitine is not usually detected in normal individuals. The elevation of 2-methylbutyrylcarnitine suggests a deficiency of a dehydrogenase specific for isobutyryl-CoA, important in the differential diagnosis of branched chain organic acidurias by analysis of urinary organic acids and acylcarnitines in plasma or dried blood spots.

Sicherheitshinweise

• Lagerklassenschlüssel: 11 - Combustible Solids
• WGK: WGK 3
• Flammpunkt (°F): Not applicable
• Flammpunkt (°C): Not applicable