72715

Glutaryl-L-carnitine lithium salt

≥98.0% (TLC)

• Sinónimos: L-Carnitine lithium glutarate
• Fórmula empírica (notación de Hill): C₁₂H₂₁NO₆ · xLi⁺
• Número CAS: 102636-82-8
• Peso molecular: 275.30 (free acid basis)
• UNSPSC Code: 41116107
• PubChem Substance ID: 329764299
• NACRES: NA.25

Propiedades

• Nombre del producto: Glutaryl-L-carnitine lithium salt, ≥98.0% (TLC)
• Quality Segment: 100
• assay: ≥98.0% (TLC)
• form: solid
• optical activity: [α]/D -20±2°, c = 1 in H₂O
• impurities: ≤10% water
• color: white to off-white
• storage temp.: 2-8°C
• SMILES string: C[N+](C)(C)C[C@H](OC(CCCC(O)=O)=O)CC([O-])=O.C
• InChI: 1S/C12H21NO6/c1-13(2,3)8-9(7-11(16)17)19-12(18)6-4-5-10(14)15/h9H,4-8H2,1-3H3,(H-,14,15,16,17)/t9-/m1/s1
• InChI key: NXJAXUYOQLTISD-SECBINFHSA-N

Descripción

Biochem/physiol Actions

Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction.

Información de seguridad

• Clase de almacenamiento: 11 - Combustible Solids
• wgk: WGK 3
• flash_point_f: Not applicable
• flash_point_c: Not applicable