Saltar al contenido
MilliporeSigma

The occurrence of gamma-glutamylphenylalanine in the urine of newborn phenylketonurics.

Clinica chimica acta; international journal of clinical chemistry (1979-06-15)
H Peck, R J Pollitt
PMID466810
RESUMEN

The urine of untreated phenylketonurics in the first weeks of life contains gamma-glutamylphenylalanine (0.07--0.69 mmol/g creatinine, 12 samples) visible on the normal 2-dimensional electrophoreto-chromatogram. This compound is less prominent or absent when urine from older untreated phenylketonurics is examined and is not seen in normal urine.

MATERIALES
Referencia del producto
Marca
Descripción del producto

Sigma-Aldrich
L-Leucine, from non-animal source, meets EP, JP, USP testing specifications, suitable for cell culture, 98.5-101.0%
Sigma-Aldrich
L-Leucine, reagent grade, ≥98% (HPLC)
Sigma-Aldrich
L-Phenylalanine, from non-animal source, meets EP, JP, USP testing specifications, suitable for cell culture, 98.5-101.0%
Sigma-Aldrich
L-Valine, from non-animal source, meets EP, JP, USP testing specifications, suitable for cell culture, 98.5-101.0%
Sigma-Aldrich
Phenylacetic acid, 99%
Sigma-Aldrich
Mandelic acid, 99%
SAFC
L-Valine
Sigma-Aldrich
17α-Hydroxyprogesterone, ≥95%
Sigma-Aldrich
Phenylacetic acid, ≥99%, FCC, FG
Sigma-Aldrich
L-Leucine, BioUltra, ≥99.5% (NT)
Sigma-Aldrich
3-Phenyllactic acid, ≥98%
Sigma-Aldrich
L-Valine, BioUltra, ≥99.5% (NT)
Sigma-Aldrich
Phenylpyruvic acid, 98%
Sigma-Aldrich
L-Leucine, 99%, FG
Sigma-Aldrich
L-(−)-3-Phenyllactic acid, 98%
Sigma-Aldrich
L-Phenylalanine, reagent grade, ≥98%
Sigma-Aldrich
3-Hydroxyphenylacetic acid, ≥99%
Sigma-Aldrich
2-Hydroxyphenylacetic acid, ReagentPlus®, 99%
Supelco
17α-Hydroxyprogesterone solution, 1.0 mg/mL in methanol, ampule of 1 mL, certified reference material, Cerilliant®
Sigma-Aldrich
L-Phenylalanine, 99%, FCC
Sigma-Aldrich
L-Valine, reagent grade, ≥98% (HPLC)
Supelco
L-Phenylalanine, Pharmaceutical Secondary Standard; Certified Reference Material
Supelco
L-Leucine, Pharmaceutical Secondary Standard; Certified Reference Material
Supelco
L-Valine, Pharmaceutical Secondary Standard; Certified Reference Material
Supelco
DL-Mandelic acid, analytical standard
Sigma-Aldrich
L-Phenylalanine, SAJ special grade, ≥99.0%
Supelco
L-Phenylalanine, certified reference material, TraceCERT®, Manufactured by: Sigma-Aldrich Production GmbH, Switzerland
Supelco
L-Valine, certified reference material, TraceCERT®, Manufactured by: Sigma-Aldrich Production GmbH, Switzerland
Supelco
L-Leucine, certified reference material, TraceCERT®, Manufactured by: Sigma-Aldrich Production GmbH, Switzerland