- Combined replacement effects of human modified β-hexosaminidase B and GM2 activator protein on GM2 gangliosidoses fibroblasts.
Combined replacement effects of human modified β-hexosaminidase B and GM2 activator protein on GM2 gangliosidoses fibroblasts.
Biochemistry and biophysics reports (2016-06-08)
Keisuke Kitakaze, Chikako Tasaki, Youichi Tajima, Takatsugu Hirokawa, Daisuke Tsuji, Hitoshi Sakuraba, Kohji Itoh
PMID28955902
RÉSUMÉ
GM2 gangliosidoses are autosomal recessive lysosomal storage diseases (LSDs) caused by mutations in the
MATÉRIAUX
Référence du produit
Marque
Description du produit
Sigma-Aldrich
Anticorps monoclonal anti-β-actine antibody produced in mouse, clone AC-74, ascites fluid
Sigma-Aldrich
Anti-GM2A antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution