04609
O-Succinyl-L-carnitine lithium salt
analytical standard
Sign Into View Organizational & Contract Pricing
All Photos(1)
About This Item
Empirical Formula (Hill Notation):
C11H19NO6 · xLi+
Molecular Weight:
261.27 (free acid basis)
UNSPSC Code:
41116107
NACRES:
NA.24
Recommended Products
![[(3R)-3-Hydroxybutyryl]-L-carnitine analytical standard](/deepweb/assets/sigmaaldrich/product/structures/658/500/ff9570f8-a346-4077-9983-d0e67400bf47/640/ff9570f8-a346-4077-9983-d0e67400bf47.png)
grade
analytical standard
Quality Level
Assay
≥94.0% (HPLC)
optical activity
[α]/D -16.0±3.0°, c = 0.1 in H2O
shelf life
limited shelf life, expiry date on the label
application(s)
clinical testing
format
neat
storage temp.
2-8°C
Biochem/physiol Actions
O-Succinyl-L-carnitine (C4DC) is a secondary metabolite that is not directly involved in the normal growth, development or reproduction of an organism.arises from. O-Succinyl-L-carnitine arises from the TCA cycle intermediate succinyl-CoA in plasma and liver. It is an O-acylcarnitine having succinyl as the acyl substituent. O-Succinyl-L-carnitine is used as biomarker for inborn metabolic deseases related to succinyl-CoA synthase function.
Storage Class Code
11 - Combustible Solids
WGK
WGK 3
Flash Point(F)
Not applicable
Flash Point(C)
Not applicable
Choose from one of the most recent versions:
Certificates of Analysis (COA)
Lot/Batch Number
Don't see the Right Version?
If you require a particular version, you can look up a specific certificate by the Lot or Batch number.
Already Own This Product?
Find documentation for the products that you have recently purchased in the Document Library.
Cristiano Rizzo et al.
Clinica chimica acta; international journal of clinical chemistry, 429, 30-33 (2013-11-26)
Methylmalonic aciduria (MMA) is one of the most frequent organic acidurias, a class of diseases caused by enzymatic defects mainly involved in the catabolism of branched-chain amino acids. Recently, mild MMA and C4-dicarboxylyl-carnitine (C4DC-C) accumulation have been reported in patients
Succinyl-CoA:acetoacetate transferase deficiency: identification of a new patient with a neonatal onset and review of the literature.
Niezen-Koning, K.E., et al.
The Journal of Pediatrics, 156, 870-873 (1997)
Our team of scientists has experience in all areas of research including Life Science, Material Science, Chemical Synthesis, Chromatography, Analytical and many others.
Contact Technical Service