FBN1
fibrillin 1
Synonymes:
ACMICD, ECTOL1, FBN, GPHYSD2, MASS, MFS1, OCTD, SGS, SSKS, WMS, WMS2
Espèce(s):
Human FBN1 (2200), Mouse Fbn1 (14118), Rat Fbn1 (83727), domestic cat FBN1 (101084882), cow FBN1 (281154), chicken FBN1 (373992), domestic guinea pig Fbn1 (100717565), Horse FBN1 (100055741), naked mole-rat Fbn1 (101718482), sheep FBN1 (101109620)
ID UniProtKB:
ID du gène:
- Human(2200) Summary: This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12 nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosynostosis syndrome. [provided by RefSeq, Jul 2008]
- Mouse(14118) fibrillin 1
- Rat(83727) fibrillin 1
- domestic cat(101084882) fibrillin 1
- cow(281154) fibrillin 1
- chicken(373992) fibrillin 1
- domestic guinea pig(100717565) fibrillin 1
- Horse(100055741) fibrillin 1
- naked mole-rat(101718482) fibrillin 1
- sheep(101109620) fibrillin 1
- dog(478293) fibrillin 1
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Antibodies
Référence du produit
Description
Espèces réactives
Application
Anticorps anti-fibrilline, clone 11C1.3, clone 11C1.3, Chemicon®, from mouse,
Espèces réactives
bovine, human, pig
Application
ELISA
immunofluorescence
immunohistochemistry
immunoprecipitation (IP)
western blot
immunofluorescence
immunohistochemistry
immunoprecipitation (IP)
western blot
Anti-FBN1 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Espèces réactives
human
Application
immunofluorescence
immunohistochemistry
immunohistochemistry
Anti-FBN1 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Espèces réactives
human
Application
immunohistochemistry
Anti-Fibrillin-1 antibody produced in rabbit, affinity isolated antibody,
Espèces réactives
human, mouse, rat
Application
ELISA
immunohistochemistry
immunohistochemistry
Monoclonal Anti-FBN1 antibody produced in mouse, Prestige Antibodies® Powered by Atlas Antibodies, clone CL0225, purified immunoglobulin, buffered aqueous glycerol solution,
Espèces réactives
human
Application
immunohistochemistry
western blot
western blot