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Merck

ATP7B

ATPase, Cu++ transporting, beta polypeptide

Sinónimos:
PWD, WC1, WD, WND
Especie:
ID UniProtKB:
ID del gen:
  • Human(540) Summary: This gene is a member of the P-type cation transport ATPase family and encodes a protein with several membrane-spanning domains, an ATPase consensus sequence, a hinge domain, a phosphorylation site, and at least 2 putative copper-binding sites. This protein functions as a monomer, exporting copper out of the cells, such as the efflux of hepatic copper into the bile. Alternate transcriptional splice variants, encoding different isoforms with distinct cellular localizations, have been characterized. Mutations in this gene have been associated with Wilson disease (WD). [provided by RefSeq, Jul 2008]
  • Mouse(11979) ATPase, Cu++ transporting, beta polypeptide
  • Rat(24218) ATPase, Cu++ transporting, beta polypeptide
  • Zebrafish(556499) ATPase, Cu++ transporting, beta polypeptide (Wilson disease)
  • sheep(443046) ATPase, Cu++ transporting, beta polypeptide
  • chicken(418879) ATPase, Cu++ transporting, beta polypeptide
  • cow(518075) ATPase, Cu++ transporting, beta polypeptide
  • domestic guinea pig(100723125) ATPase, Cu++ transporting, beta polypeptide
  • Domestic Rabbit(100344865) ATPase, Cu++ transporting, beta polypeptide
  • domestic cat(101091495) ATPase, Cu++ transporting, beta polypeptide
  • dog(476903) ATPase, Cu++ transporting, beta polypeptide
  • naked mole-rat(101712944) ATPase, Cu++ transporting, beta polypeptide
  • Horse(100052751) ATPase, Cu++ transporting, beta polypeptide

Custom & Knockdown Gene Products

Antibodies

Número de producto
Descripción
Reactividad de especies
Aplicación
KD-Validated Anti ATP7B Antibody, clone 23GB3945, Rabbit Monoclonal, clone 23GB3945, recombinant rabbit monoclonal, expressed in HEK293 cells,
Reactividad de especies
human
Aplicación
flow cytometry
immunofluorescence

western blot

esiRNA

Número de producto
Descripción
Especie
MISSION® esiRNA, targeting human ATP7B,
Especie
human
MISSION® esiRNA, targeting mouse Atp7b,
Especie
mouse